Table 83:Vascalar Malformations/Lesions

Table 83: Syndromes associated with oral and paraoral vascular malformations.

With Hemangiomas:

• Bannayan-Riley-Ruvalcaba syndrome
• Beckwith-Wiedemann syndrome
• Disseminated hemangiomatosis
• Epidermal nevus syndrome
• Klippel-Trenaunay-Weber syndrome
• Maffucci syndrome (enchondromatosis and hemangiomatosis)
• Multiple angiomas with thrombocytopenia
• Proteus syndrome
• Pseudoxanthoma elasticum
• Sotos syndrome (cerebral gigantism)
• Sturge-Weber angiomatosis (Sturge-Weber syndrome)
• Tuberous sclerosis
• von Recklinghausen neurofibromatosis

With Telangiectasias or Varicosities:

• Acrolabial telangiectasia
• Bean syndrome (blue rubber bleb nevus syndrome)
• Coats disease (telangiectatic retinal detachment)
• CREST syndrome (Calcinosis, Raynaud's phenomenon, Esophageal dysfunction, Sclerodactyly, Telangiectasia syndrome)
• Cutis marmorata telangiectatica congenita
• Fabry syndrome (angiokeratoma corporis diffusum universale)
• Hereditary hemorrhagic telangiectasia (Osler-Rendu-Parkes Weber syndrome)
• Kasabach-Merritt syndrome
• Scleroderma